A novel human iPSC model of COL4A1/A2 small vessel disease unveils a key pathogenic role of matrix metalloproteinases in extracellular matrix abnormalities

Al-Thani M., Goodwin-Trotman M., Bell S., Patel K., Fleming LK., Vilain C., Abramowicz M., Allan SM., Wang T., Cader Z., Horsburgh K., Van Agtmael T., Sinha S., Markus HS., Granata A.

DOI

10.1101/2023.02.23.529680

Type

Preprint

Publication Date

23/02/2023

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